1 - Serviço de Radiologia, Hospital Dona Estefânia, Centro Hospitalar Universitário de Lisboa Central, Lisboa;
2 - Serviço de Radiologia, Hospital São José, Centro Hospitalar Universitário de Lisboa Central, Lisboa;
- Publicação como “Images in Clinical Radiology” - Journal of the Belgian Society of Radiology
Case report: A 2-year-old boy presented with a nine-month history of progressively growing cervicothoracic painful mass, without associated inflammatory signs, respiratory distress, or constitutional symptoms. An ultrasound was performed, which showed a bulky hyperechoic and only slightly heterogeneous solid mass occupying the upper left hemithorax without calcifications or Doppler signal. CT and MRI were performed which were consistent with a lipomatous tumour. The patient underwent a thoracotomy and complete free margin resection of the tumour. Histopathological results showed mainly adipocytes and lipoblasts at varying stages of maturation consistent with mediastinal lipoblastoma. Two years after the procedure, no signs of recurrence were found
Teaching point: Lipoblastoma should be considered in the differential diagnosis of painful rapidly growing fatty mass within the mediastinum in infants or young children under three years old.
Palavras Chave:Lipoblastoma, Mass, Mediastinal, Paediatric