1 - Serviço de Radiologia, Centro Hospitalar de Lisboa Ocidental, Lisboa
2 - Serviço de Radiologia, Hospital Dona Estefânia, Centro Hospitalar Universitário de Lisboa Central, Lisboa
3 - Serviço de Radiologia, Hospital Dona Estefânia, Centro Hospitalar Universitário de Lisboa Central, Lisboa
4 - Serviço de Radiologia, Hospital Dona Estefânia, Centro Hospitalar Universitário de Lisboa Central, Lisboa
- Publicação sob a forma de poster electrónico no International Pediatric Radiology Congress 2021 (11/10/2021-15/10/2021)
Resumo:
Objective: The purpose of this presentation is to demonstrate the imaging findings of various types of congenital portosystemic shunts and therefore allow for their recognition when characteristic features are present.
Material and Methods: Imaging features of these congenital malformations are presented and discussed, according to a review of the literature, and illustrated by cases from our institutions.
Results: Congenital portosystemic shunts are rare developmental anomalies resulting in diversion of portal flow to the systemic circulation. Congenital portosystemic venous shunts are best classified as: intrahepatic and extrahepatic. Most often, the diagnosis is made primarily with Doppler ultrasonography. Computed tomographic angiography and magnetic resonance angiography are used for further classification of the shunt and assessment of accompanying anomalies.
Conclusions: Despite the rarity of congenital abnormal communications between the portal and systemic venous circulation, radiologists have to consider this diagnosis in children who present with nonspecific liver dysfunction. Familiarity with the characteristic features are useful for an early diagnosis and to choose the best therapeutic approach.
Palavras Chave: Congénito, Pediatria, Portossistémico, Radiologia, Shunt