1 - Serviço de Pediatria; Centro Hospitalar Universitário do Algarve; Algarve
2 - Área da Mulher, Criança e Adolescente; Hospital de Dona Estefânia; Centro Hospitalar de Lisboa Central, Lisboa
3 - Unidade de Nefrologia Pediátrica; Hospital de Dona Estefânia; Área da Mulher, Criança e Adolescente; Centro Hospitalar de Lisboa Central, Lisboa
4 – Unidade de Cuidados Intensivos Pediátricos; Hospital de Dona Estefânia; Área da Mulher, Criança e Adolescente; Centro Hospitalar de Lisboa Central, Lisboa
5 – Unidade de Cirurgia Pediátrica; Hospital de Dona Estefânia; Área da Mulher, Criança e Adolescente; Centro Hospitalar de Lisboa Central, Lisboa
- Portuguese Journal of Nephrology and Hypertension, Vol. 32, N. 2 (publicação em versão integral)
Pheochromocytoma and renal artery stenosis are surgically treatable causes of hypertension. Although rare, the coexistence of pheochromocytoma and renal artery stenosis has been described in case reports. Common pathophysiological mechanisms other than extrinsic compression may be involved in this association, such as catecholamine-induced vasospasm. The early recognition of the association of pheochromocytoma with renal artery stenosis is essential for appropriate treatment planning. We present the case of a previously healthy ten-year-old boy who presented with hypertensive encephalopathy, tachycardia and diaphoresis. Hypertension was found to be secondary to a catecholamine-producing tumour associated with coexisting renal artery stenosis. Hypertension resolved a few months after successful pheochromocytoma excision, without renal artery revascularization.
Palavras Chave: child; hypertension; pheochromocytoma; posterior reversible encephalopathy syndrome; renal artery stenosis.