1 - Serviço de Pediatria - Hospital Doutor Nélio Mendonça, Funchal.
2 - Unidade de Gastrenterologia Pediátrica, CHULC - Hospital de Dona Estefânia
BMJ Case Rep. 2018 Dec 13;11(1). pii: e227888. doi: 10.1136/bcr-2018-227888
Publicação em versão integral em revista indexada
Introduction: Autoimmune pancreatitis (AIP) is a rare entity that is extremely uncommon in children. Its diagnosis is also a clinical challenge. This form of chronic pancreatitis often presents itself with obstructive jaundice and/or a pancreatic mass and it is sometimes misdiagnosed as pancreatic cancer.
Case presentation: We describe the case of a 13-year-old boy with obstructive jaundice and a 4 cm mass in the head of the pancreas that was diagnosed as AIP with associated ulcerative colitis
Learning points: (1) Autoimmune pancreatitis (AIP) rarely occurs in children and is a distinctive subtype of pancreatitis. (2) Paediatric autoimmune pancreatitis (P-AIP) should be taken into consideration in the differential diagnosis in children with a pancreatic enlargement. (3) Most children with AIP present with abdominal pain and/or obstructive jaundice. (4) The diagnosis of P-AIP can be made based on the combination of clinical presentation and imaging findings, possibly complemented by histopathological findings. (5) First choice treatment in P-AIP are steroids. However, some patients may have symptom resolution without any treatment.
Key words: autoimmune pancreatitis, obstructive jaundice, pancreatic mass, ulcerative colitis.